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[2000] 14. BongWoo Lee, Joong-Seok Seo, Tae-Jung Kwon, Won-Tae Lee |
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Poster :
Date : 09-12-23 17:48
Hit : 1095
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Publication; issue : 2000 Year 24 Vol 1 iss 92 p
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(2.8M), Down : 50, 2009-12-23 17:48:07 | |
A Sudden Death in a Patient with Neurofibromatosis.
Korean J Leg Med. 2000 May;24(1):92-97. Korean.
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Department of Forensic Medicine, National Institute of Scientific Investigation, Korea.
Neurofibromatosis type1(von Recklinghausen's disease) is characterized by multiple skin tumors and abnormal cutaneous pigmentation(cafe au lait spots). Unlikely the solitary neurofibroma, those encountered in von Recklinghausen's disease may cause significant morbidity. The vasculopathy, although poorly recognized manifestation of von Recklinghausen's neurofibromatosis is a major cause of fatal cases. One of its most dramatic presentation is the spontaneous hemothorax. We report a case of Von Recklinghausen's disease with multiple neurofibromatosis accompanying intrathoracic hemorrhage due to vascular rupture, which is the first legal autopsy case in korea.
Key words: Neurofibromatosis type 1, hemothorax
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